سندرم شبه اسکلرودرمی معرفی یک بیمار نادر (سندرم ورنر)
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Abstract:
Scleroderma-like syndromes are a group of disorders that mimic systemic sclerosis. Werner’s syndrome is a genetically inherited syndrome that can be misdiagnosed as systemic scleroderomia. The syndrome is charachterized by sclerosis or stiffening of the skin, progeris, bilatera l juvenile cataract, endocrinopathies, premature coronary artery disease, alopecia, nail plate changes, hyperpigmentation and susceptibility to malignant neoplasms. We describe a case of Werner’s syndrome who presented with chronic leg ulcer and was misdiagnosed as systemic sclerosis for many years. We stopped unnecessary treatments and chronic leg ulcer was biopsied to rule out of skin cancer and managed locally by antibiotics and daily care.
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Journal title
volume 9 issue 32
pages 637- 642
publication date 2003-03
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